Clear Cell Sarcoma: A Case Report and Review of Literature

  • Alireza Abdollahi Department of Pathology, Faculty of Medicine, Tehran University of Medical Sciences, Tehran, Iran
  • Fatemeh Khatami Chronic Diseases Research Center, Endocrinology and Metabolism Population Sciences Institute, Tehran University of Medical Sciences, Tehran, Iran
  • Seyed Mohammad Tavangar Chronic Diseases Research Center, Endocrinology and Metabolism Population Sciences Institute, Tehran University of Medical Sciences, Tehran, Iran Department of Pathology, Shariati Hospital, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran
Keywords: Clear cell sarcoma, Soft tissues, Malignant melanoma, Melanoma of soft part

Abstract

Clear cell sarcoma (CCS), a deep-rooted tumor with a predilection for lower extremities, has a proclivity to involve the tendons and aponeuroses. This sarcoma is seen predominantly around the foot and ankle region. Diagnosis is mainly finalized using histological and immunohistochemical assessment. The main treatment strategy is surgery followed by chemotherapy. An erratic challenge is posed by histological similarity and immunohistochemical overlap to the diagnosis and distinguishing of clear cell sarcoma from primary or metastatic malignant melanoma (MM) which is more common. Here, we described a CCS case located in the left leg of a 37-year-old male patient.

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Published
2018-01-05
How to Cite
1.
Abdollahi A, Khatami F, Tavangar SM. Clear Cell Sarcoma: A Case Report and Review of Literature. ijhoscr. 12(1):65-8.
Section
Case Report(s)