Case Report

Rare Presentation of Refractory Thrombotic Thrombocytopenic Purpura: Jejunal Stricture

Abstract

Thrombotic thrombocytopenic purpura is a rare thrombotic disease characterized by episodes of thrombocytopenia and microangiopathic hemolytic anemia due to disseminated microvascular thrombosis. Thrombotic thrombocytopenic purpura was first described in 1924 by Moschowitz as a disease presenting with a pentad of signs and symptoms (anemia, thrombocytopenia, fever, hemiparesis and hematuria). Previous studies have described atypical manifestations of thrombotic thrombocytopenic purpura such as hemolysis, anemia and thrombosis.

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IssueVol 11, No 4 (2017) QRcode
SectionCase Report(s)
Keywords
TTP Chron’s- disease
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Creative Commons License This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.
How to Cite
1.
Abeysundara P, Atukorala I, C. Dalpatadu K, Balendran K, S. A. Dilrukshi M, O Fernando G. Rare Presentation of Refractory Thrombotic Thrombocytopenic Purpura: Jejunal Stricture. Int J Hematol Oncol Stem Cell Res. 2017;11(4):293-295.