Case Report

Clear Cell Sarcoma: A Case Report and Review of Literature


Clear cell sarcoma (CCS), a deep-rooted tumor with a predilection for lower extremities, has a proclivity to involve the tendons and aponeuroses. This sarcoma is seen predominantly around the foot and ankle region. Diagnosis is mainly finalized using histological and immunohistochemical assessment. The main treatment strategy is surgery followed by chemotherapy. An erratic challenge is posed by histological similarity and immunohistochemical overlap to the diagnosis and distinguishing of clear cell sarcoma from primary or metastatic malignant melanoma (MM) which is more common. Here, we described a CCS case located in the left leg of a 37-year-old male patient.

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IssueVol 12, No 1 (2018) QRcode
SectionCase Report(s)
Clear cell sarcoma Soft tissues Malignant melanoma Melanoma of soft part

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How to Cite
Abdollahi A, Khatami F, Tavangar SM. Clear Cell Sarcoma: A Case Report and Review of Literature. Int J Hematol Oncol Stem Cell Res. 2018;12(1):65-68.