Articles

Successful Hemodialysis and Renal Transplantation in Combined Factors of V and VIII Deficiencies

Abstract

Introduction: The prevalence of rare bleeding disorders, including combined factor V+VIII deficiency are higher in Iran than in developed countries. There are only a few reports which have been written concerning kidney transplantation in the patients suffering from these disorders.
Case report: A 22-year old girl, with a known case of combined factor V+VIII deficiency, a history of bladder stone surgery, postoperative bleeding and a need for hemodialysis due to renal failure was admitted for allograft kidney transplantation. The patient received fresh-frozen plasma and factor VIII, according to individualized protocol before, during and after the course of the transplantation. The function of the grafted kidney was very good nine months post-transplantation.
Discussion: Only heparin was used during hemodialysis. It has been shown that allograft kidney transplantation can be performed in rare bleeding disorders with good replacement therapy without any complications.

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IssueVol 4, No 1 (2010) QRcode
SectionArticles
Keywords
Rare Bleeding Disorders Combined Factor V VIII Deficiency Kidney Transplantation
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Creative Commons License This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License.
How to Cite
1.
Naderi A, Ebadzadeh M, Azmandyan J, Fayazfar R, Ahmadi E, Rikhtehgaran Tehrani A. Successful Hemodialysis and Renal Transplantation in Combined Factors of V and VIII Deficiencies. Int J Hematol Oncol Stem Cell Res. 1;4(1):28-30.